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Abstract Present Situation: Research investigation deals with nursing care of the child with glycogen storage disease type I., as well as its diagnosis, nutritional management and complications. Glycogen storage disease (GSD) belongs among rare hereditary metabolic disorders. There are several types of GSD, divided into hepatic, myopathic and generalized forms. Early diagnosis is essential for effective treatment of the disease, the signs and symptoms of which first appear in babies soon after birth. The aim of this thesis was to describe the nursing care of the child with glycogen storage disease type I and identify the problems parents of affected children have to face. Methodology: Quantitative research method was used for empirical part of the thesis. The data collection was carried out through In-depth interviews with paediatric-ward nurses and a mother of the child with GSD type I. All interviews were audio recorded, transcribed and coded using paper-and-pencil method and finally categorized. The research sample consisted of nine paediatric-ward nurses and the mother taking care of the child with glycogen storage disease type I, also known as Gierke's disease. Selection of the sample was purposive and its size was determined by theoretical saturation of data. Results: Nursing care of children with glycogenosis type I requires regular feedings of a special diet enriched with corn starch substances to maintain the level of glycemia in the physiological range and to avoid dangerous hypoglycaemia. Problems for nursing staff mainly involve the unstable health condition of a child, fluctuating glycemia levels and limited knowledge of the disease. Parents not only worry about potential health complications of their child but they are also concerned about technical problems with feeding aids, poor recognition of hypoglycaemia and the child's mental welfare. The disease presents increased physical and emotional demands on the patient and their family. Conclusions and recommendations for practice: The thesis presents an outlook on the issue of paediatric-ward nursing care of the child with glycogen storage disease type I and indicates the common problems of the family with a child affected by the disease. The effort was to thoroughly understand the nature of the disease and to identify basic nursing care procedures which can benefit nurses in other facilities dealing with the same diagnosis. The results of the research will be presented in the magazine "Pediatrie pro praxi" in the nursing section.

Our nutrition significantly influences our healthy development, quality of our life and mainly our health condition in general. No one discredits today the fact that faults in our nutrition result in emergence and further development of illnesses. On the contrary there is enough evidence on a very positive effect of changes in nutrition on a single person, group of people or the whole generation. The objective of my diploma thesis was to find out the quality of food consumed by school-age pupils. I used quantitative research for my diploma work. Data aquisition was carried out in the form of question-forms in order to address as many respondents as possible. Questions {--}forms were alloted for pupils at primary schools. There were three hypotheses. Hypothesis 1: Czech pupils consume fuel food overly rich in sugars. This hypothesis was proved.. Hypothesis 2: Czech children consume less than 30g of fibre a day. The hypothesis was also proved. Hypothesis 3: In pupils´ ingestion of food there is more than 300 mg of cholesterol a day. This hypothesis was not proved at all. It is obvious from the results that Czech pupils do not consume recommended healthy food.The results of my diploma thesis could be used as a basis for improvement in eating habits of school-age children. Bad parental approach to healthy nutrition is one of the key factors that contribute to the growth of obesity and other serious deseases. Parents should be informed about bad and wrong eating habits of their children and at the same time they should be advised how to make a healthy and suitable daily menu for their children. Parents could be kept informed by various informative leaflets distributed at schools or there might be held special lectures aimed at this broad issue. Because we are one of the states where obesity is a big problem even for a younger population. I am sure that all these activities could be useful for gradual improvement in changes concerning bad unhealthy eating habits of pupils, their better health condition and even restricition of obesity.