TITLE: Two-cycle studies of the English language at the Faculty of Education of Charles University in Prague: opinions of students and teachers AUTHOR: Bc. Jiřina Piškulová DEPARTMENT: Department of Education SUPERVISOR: PhDr. RNDr. Hana Voňková, Ph.D. et Ph.D. ABSTRACT: As a consequence of the Bologna process, five-year master's teacher education programme has been divided into three-year bachelor's and consecutively two-year master's programme. The aim of the thesis is to reflect on the changes which have come with the implementation of the structured studies in teacher education programme in the Department of English Language and Literature, Faculty of Education, Charles University in Prague and to present survey results about the opinions of both the students and the academic staff at the Department. In the theoretical part of the work the Bologna process is introduced - its goals, development and the reaction on its introduction in the Czech Republic. The concept of the teacher education from before the Bologna process is described. A comparison has been drawn to the teacher education programme in Germany. In the practical part an analysis of the study plans from before and after the Bologna process has been made and then the data from a questionnaire survey are presented and interpreted. It has shown...

L'IRM conventionnelle est considérée comme l'outil non invasif de référence pour le diagnostic, le bilan pré-thérapeutique et le suivi post-thérapeutique des tumeurs cérébrales de l'enfant et de l'adulte. Cependant, en raison de son manque de spécificité aussi bien pour certains diagnostics différentiels que pour l'évaluation de la réponse radiologique, différentes modalités d'IRM sont aujourd'hui ajoutées à l'examen conventionnel dans le but d'affiner l'exploration de ces tumeurs. L'utilisation d'une modalité unique n'est malgré tout pas suffisante pour établir une évaluation diagnostique ou pronostique optimale des tumeurs cérébrales. C'est pourquoi nous nous sommes intéressés à la combinaison de données issues des différentes modalités d'IRM dans le but d'obtenir une meilleure caractérisation, en termes de différenciation et d'évolutivité de ces néoplasmes. Dans ce contexte, nous avons investigué par IRM multimodale 1) les tumeurs épileptogènes de l'enfant, pour lesquelles il est crucial de déterminer le diagnostic préopératoire afin d'aider à la prise en charge chirurgicale ; 2) les tumeurs oligodendrogliales de l'adulte, difficilement distinguables et dont les décisions thérapeutiques reposent sur la détermination du grade et du profil moléculaire ; et enfin 3) la réponse des glioblastomes aux traitements anti-angiogéniques. / Conventional MRI is considered as the gold standard method for the non-invasive diagnosis, pretherapeutic assessment and follow-up of brain tumors in adults and in children. However, due to its lack of specificity for both differential diagnosis and evaluation of the response to treatment, several MR modalities are now added to the conventional exam in order to refine the exploration of these tumors. The use of a single modality is however not yet sufficient to establish an accurate diagnosis or prognosis for brain tumors. For this reason, we were interested in the combination of data from different MR modalities in order to obtain a better characterization of these neoplasms. In this context, we used multimodal MRI to investigate 1) pediatric epileptogenic tumors, for which it is crucial to establish a preoperative diagnosis in order to make appropriate surgical and therapeutic decisions; 2) oligodendroglial tumors in adults, hardly distinguishable and which therapeutic decisions are mainly based on the determination of the tumoral grade and molecular profile; and 3) the response of glioblastoma to anti-angiogenic treatments. Through this work, we have shown that the association of different imaging modalities provides a significant contribution to the differential pre-therapeutic diagnosis of epileptogenic brain lesions in children and also of oligodendroglial tumors in adults as well as a support for the early assessment of tumoral response to anti-angiogenic therapies.

Abstrakt I världen ökar ohälsa och sjukdom markant relaterat till dåliga levnadsvanor som exempelvis otillräcklig fysisk aktivitet. Fysisk aktivitet definieras som alla former av planerad fysisk aktivitet som ger ökad energiomsättning och som påverkar hälsan positivt där målet är att öka prestationsförmågan. Syftet med denna studie var att beskriva personers upplevelser av fysisk aktivitet på recept (FaR). Kunskap i dessa nämnda områden kan leda till minskade livsstilsrelaterade sjukdomar såsom fetma, övervikt, diabetes och hjärt-kärlsjukdomar samt t.ex. minska viktökning och stillasittande. Det i sig påverkar folkhälsan och samhället positivt, även så kostnadsmässigt. Metoden hade en kvalitativ ansats. Data samlades in genom semistrukturerade intervjuer med tio personer som levde både i glesbygd i norr och i storstad i söder. Analysen som genomfördes med kvalitativ innehållsanalys resulterade i fem huvudkategorier: En känsla av bättre välbefinnande; Ökad motivation till förändring; En berg- och dalbana av känslor; Behov av att få uppföljande samtal; Leder till ett positivt resultat. Resultatet visade att personer började må bättre psykiskt och fysisk samtidigt som de blev piggare i kroppen och fick en mycket positivare inställning till livet. Det var viktigt att ha motivation till förändring för att lyckas med en livsstilsförändring. Det var en känslomässig och laddad process och uppföljande samtal var mycket viktigt. FaR beskrevs som en positiv upplevelse för deltagarna och gav goda resultat på kort tid. Konklusion Resultatet visar att FaR är ett bra verktygför att uppnå bättre hälsa psykiskt och fysiskt samt i flera andra aspekter. Sjukvårdpersonal har en viktig uppgift när det gäller stöd, motivation och uppföljning. Det kan vara känslomässigt och laddat när grunden till att ta hjälp av FaR ofta kan vara påfrestande mentalt. Det upplevdes som negativt att ej ha tillgång till uppföljning.

Syftet med denna studie var att utvärdera behandling med hjälp av elektropalatografi (EPG) och portabel träningsenhet (PTU) hos en person med kvarstående artikulationsproblem. Försökspersonen var en vuxen man med medfödd hemifacial mikrosomi och mikrognati som tidigare genomfört konventionell talträning. En kvasiexperimentell, prospektiv, kontrollerad single subjekt A-B-A design användes. Försökspersonen hade vid träningsstart en tillbakadragen artikulation av /t/ och /d/ till velart/uvulart artikulationsställe med kvarstående svårighet att göra sitt tal förståeligt för sina samtalspartners.  Behandlingseffekten utvärderades genom instrumentell EPG analys av /t/ i enstaka ord före och efter behandling. Analysen visade signifikanta behandlingsresultat där en fortgående förbättring av produktionen av /t/ i medial och final position skedde även fyra år efter avslutad behandling. Perceptuell lyssnarbedömning av tränade och otränade lyssnare uppvisade signifikant förbättrad skattning av t-likhet av målljudet /t/ i medial och final position över tid. Ett mycket svagt samband sågs mellan perceptuell skattning av t-likhet och de analyserade EPG-värdena. Lyssnarskattningen av spontantalet visade en förbättring av förståelighet vid kontroll 4 år efter avslutad träning. Utvärderingen bekräftar tidigare forskning och visar att talträning med EPG är ett effektivt sätt att ge visuell återkoppling i försök att etablera ett korrekt artikulationsmönster, förbättrat tal och ökad förståelighet. Detta provades i föreliggande studie och även om resultaten inte var entydiga, antyddes att metoden kan vara långsiktigt framgångsrik vid sedan lång tid väl etablerade talavvikelser utan tecken på förändring spontant eller efter tidigare träning utan visuell återkoppling. En viktig erfarenhet är således att planera långsiktigt och invänta automatisering av nya artikulationsrörelser som har lång etableringsfas. Träning med EPG föreslås kunna erbjudas vuxna personer med kvarstående artikulationsavvikelser där konventionell träning inte har kunnat ge önskvärda resultat. Nyckelord: Elektropalatografi, behandlingseffekt, hemifacial mikrosomi, artikulationsstörning, långtidsuppföljning, förståelighet / The aim of this study was to evaluate speech therapy using electropalatography (EPG) and portable training unit (PTU) in a subject with persistent articulation errors. The participant was a male adult with congenital hemifacial microsomia and micrognathia who previously had received conventional speech therapy. The subject had a retracted, velar/ uvular articulation of dental plosives with difficulty making speech understandable to listeners. A quasi-experimental prospective, controlled single-subject ABA design was used. Treatment efficacy was assessed by instrumental EPG analysis of  /t/ in single words before and after treatment and showed significant treatment results with a continuing improvement in the production of  /t/ in medial and final position even four years after completion of treatment. Perceptual listen assessment of trained and untrained listeners showed significantly improved estimation of the target /t/ in medial and final position over time. A very weak association was found between the perceptual estimation of t-likeness and the analyzed EPG values. Listener rating of spontaneous speech showed an improvement in intelligibility 4 years after completing training. The evaluation confirms previous research showing that speech therapy with EPG seems effective for providing visual feedback in the attempt to establish a correct articulation pattern, improved speech and enhanced intelligibility. This was investigated in the present study and although the results were not unambiguous, it was indicated that the method can be successful at long persisting well established articulation errors without signs of spontaneous change or after previous training without visual feedback. An important experience is to plan long term and wait for the automation of the new articulation movements that have a long establishment phase. Training with EPG is proposed to be offered to adults with persistent articulation disorders for which conventional therapy has been unable to provide desirable results. Keywords:  Electropalatography, treatment effect, hemifacial microsomia, articulation disorder, long- term follow- up, intelligibility

Thesis objectives: The thesis deals with the comparison of wound healing management in acute and subsequent care. The theoretical part presents the knowledge of acute and chronic wounds, wound healing and their phases. Furthermore, the thesis deals with methods of wound treatment. The last chapter of the theoretical part deals with management and the role of a nurse in caring for a patient with a wound. In the empirical part, the first goal was to find out whether nurses from the Hradec Králové Region hospitals know the division and types of wounds. The second goal was to map out the possibilities for nurses to heal wounds. Another aim was to compare the differences between wound healing in acute and subsequent care. The fourth goal mapped the knowledge of nurses about wound healing materials. The following aim was to find out which materials for wound care are available at the hospital of the Hradec Králové Region. The sixth goal was to compare the economic and time-consuming wound healing at the acute and aftercare departments. The last goal of the thesis is to elaborate a seminar within the framework of lifelong education of general nurses on the topic of effective wound healing. Five hypotheses and two research questions were formulated to meet the goals of the thesis. Method for achieving the objectives: The set goals were achieved through quantitative questionnaire research and qualitative observation and interview research, which were chosen to complement the results. The sample included general nurses working in the internal department, the surgical department, the intensive care unit, the anesthesiology-resuscitation department and the aftercare departments in the hospitals of the Hradec Králové region. The total number of respondents was 120. Scientific benefits of the thesis: Overall research shows that nurses have sufficient knowledge of wounds and their treatment, but deficiencies in some areas are still evident. Furthermore, the research shows that nurses do not have enough therapeutic material to work on their workplaces. The interviewed group of general nurses said they think that modern dressing materials have a positive effect on wound healing. The results of the work can be used for practice, in hospital and other health care facilities to improve wound healing. The findings and conclusions: In the tracked file, we verified that the length of treatment of wounds on beds of acute and subsequent care differs (p = 0.002); the results show that the average time of wound dressing is prolonged in subsequent care. Conversely, the availability of dressing materials in the respective departments did not differ (p = 0.159). Furthermore, we found that the economic intensity of the after-care beds is lower, despite the fact that more wound dressings are done than in the acute care.

Cette recherche a eu lieu au Qatar, pays du Golfe persique, où une vaste réforme du système éducatif est entreprise. Notre premier objectif dans cette étude a été d'examiner l'évolution des programmes de formation continue des enseignants des écoles dites indépendantes tels qu'offerts par la seule université nationale, Qatar University, et précisément par le College of Education (CED). Notre intérêt pour les programmes du CED est qu'ils y ont introduit progressivement un processus de suivi sur le terrain des pratiques. Notre deuxième objectif a été d'étudier les changements qu'ont pu apporter le suivi appliqué à l'un des programmes de formation continue en 2009-10 au niveau des pratiques d'enseignement et de la motivation et participation des élèves en classe. La collecte d'information s'est basée sur des documents, des questionnaires d'évaluation d'ateliers et de sessions de suivi, des observations de classes et des entretiens. Les résultats ont montré que le processus de suivi organisé au sein du programme de formation continue a amélioré les performances des enseignants et la participation des élèves en classe, montrant aussi la nécessité d'avoir une gestion pédagogique au niveau du leadership et des enseignants d'une part, et la nécessité de renforcer la coopération entre écoles et universités d'autre part. Par contre, l'effet escompté sur l'orientation professionnelle des élèves n'a pu être confirmé. Les résultats ont permis de faire quelques recommandations pour d'autres recherches, entre autres une étude qui examinerait l'effet­ établissement pour le développement d'une culture d'organisation apprenante et une autre étude sur un partenariat écoles-universités. / This research was done in the State of Qatar, located in the Gulf Region where a substantial reform begun few years ago. The first objective of this study was to explore the evolution of teachers' professional development programs (PD) offered by the sole national university in the country, Qatar University, and mainly by the College of Education (CED), to the so called Independent Schools. Our interest was specifically related to the progressive introduction of a follow-up process in CED professional development programs. The second objective was to study changes that the follow-up process could have carried out regarding independent school teachers’ practices and students' motivation and participation in class. Data were collected through documents, interviews, questionnaires and class observations. The results show that the follow-up process as planned within the PD program improved teachers’ performances to a good extent as well as students participation in class; results also show the need to reinforce instructional leadership and teachers’ effect on learning on one side, and the need to strengthen the cooperation between the schools and the university on the other side. However, the effect on students' future orientations could not be confirmed. The findings of this study helped to draw conclusions and provide a base for recommendations for further research such as the impact of instructional leadership on the development of a learning organization culture, and partnership between schools and universities.

Introduction - Quel est le modèle de suivi à long terme adapté aux attentes et besoins des jeunes adultes guéris d’un cancer dans l’enfance ? Méthode - Cette étude a pour objectif d’évaluer l’impact sur la santé de jeunes adultes guéris d’un cancer pédiatrique d’un modèle de suivi associant auto-questionnaire et consultation médicale. De jeunes adultes ayant eu un cancer entre 1987 et 1992 en Rhône-Alpes-Auvergne ont été vus en consultation médicale et psychologique de Suivi A Long Terme (SALTO), précédée et suivie d’un auto-questionnaire. De plus, la capacité d’adaptation de leur système nerveux autonome (SNA) a été évaluée afin de déterminer les caractéristiques des sujets dont le SNA était altéré. Résultats - 207 jeunes adultes ont rempli un questionnaire pré-consultation et 197 ont déclaré avoir de nombreuses séquelles, en moyenne 3,4 séquelles, ce qui a été confirmé par l’observation médicale faite chez les 150 consultants (2,6 séquelles observées/sujet). Après la consultation, près de 70% des sujets ont modifié leur nombre de séquelles déclarées. Aucune caractéristique particulière n’a pu être clairement mise en évidence quant aux personnes ayant une capacité de régulation du SNA altérée mais une relation significative a été établie entre SNA altéré et observation d’une séquelle cardiovasculaire (P=0,049). Une enquête de satisfaction a montré une opinion très favorable à la consultation SALTO. Environ 80% des sujets présentant un trouble psychiatrique au moment de la consultation ne bénéficiaient d’aucun suivi psychologique.Conclusion - Un suivi à long terme des jeunes adultes guéris d’un cancer dans l’enfance est nécessaire, faisable et répond à une demande réelle / Introduction - What is the model of long-term follow-up adapted to the expectations and needs of youngadults cured of a childhood cancer? Method – The aim of this study was to estimate the impact of a long-term follow-up care (LTFU) associated self-questionnaire and medical consultation, on the health of young adult survivors of childhood cancer. Young adults with childhood cancer between 1987 and 1992 in Rhône-Alpes-Auvergne were seen during a LTFU medical and psychological consultation (SALTO), which was preceded and followed by a self-questionnaire. Furthermore, the capacity of adaptation of their autonomous nervous system (ANS) was estimated to determine the characteristics of the subjects whose ANS was altered. Results - 207 young adults completed a questionnaire before consultation and 197 of them declared having sequalae, on average each self-reported 3.4 late effects, which was confirmed by a medical observation made at 150 consultations (mean 2.6 observed late effects/subject). After the consultation, about 70 % of the subjects modified their number of self-reported late effects. No particular characteristic was clearly highlighted in people with an altered capacity of ANS regulation but a significant relationship was established between altered ANS and cardiovascular complication (P=0,049). A satisfaction survey showed a very favorable opinion about the SALTO consultation. Approximately 80% of the subjects presenting a psychiatric disorder at the time of the consultation had received no psychological follow-up at this time. Conclusion - Long-term follow-up of young adult survivors of a childhood cancer is necessary, feasible and answers a real need

Undersökaren har studerat hur företag X skulle kunna förmå sina kunder att bli tydligare i sin kravställan och i förlängningen kvalitetssäkra sina konsulttjänster. Syftet med studien har varit att undersöka hur företag X kan skapa en röd tråd där kundernas krav och förväntningar identifieras, infrias och följs upp. Studien har svarat på följande frågeställningar: Vad definierar en kvalitativ konsulttjänst? Hur kan kunderna förmedla sina krav och förväntningar? Hur kan uppföljning av kundnöjdhet se ut? Hur kan arbetssätten följas upp? Rapporten är en fallstudie som består av kvalitativa data som samlats in genom erhållna intervjuer och genomförande av en workshop. Resultatet visar att kunden är i fokus och kvalité för företag X innebär en nöjd kund genom exempelvis leverans av efterfrågad produkt i tid till rätt pris, merförsäljning och att kundens framgång är företag X framgång. De olika respondenterna i urvalsgrupperna har idag olika arbetssätt och metoder som används för att ta reda på kundens krav och förväntningar. Kunderna tillfrågas om de vill fylla i en kundenkät vilket de relativt sällan vill. Det finns en processägare för kunduppföljningarna men processen är inte förankrad i alla led genom organisationen uppifrån och ned. Ett förbättringsområde i företagets process med kunduppföljning har identifierats, idag används två enkäter med olika skalor, där den ena enkäten ska användas enligt företagets kvalitetsledningssystem och kvalitetsmålen beräknas på den andra enkäten. Studiens slutsatser har renderat i att ett led i att kvalitetssäkra konsulttjänsterna är att identifiera kundens uttalade, underförstådda och omedvetna behov där det sistnämnda har stor betydelse för upplevelsen av kundnöjdhet. Kundens krav och förväntningar kan tänkas identifieras genom SPIN modellen. Uppföljning av kundnöjdhet bör byggas på kundens kritiska faktorer, CTQ. Arbetssätten kan följas upp genom hörnstensmodellen där alla delar skapar en helhet i offensiv kvalitetsutveckling. / The investigator has studied how company X could induce its customers to become clearer in their demands and in the long run quality assure their consulting services. The purpose of the study has been to investigate how company X can create a red thread in which the customers' requirements and expectations are identified, fulfilled and followed up. The goal for company X is to provide quality consulting services that generate the greatest possible customer satisfaction. The study has answered the following questions: What does a qualitative consulting service de-fine? How can customers more clearly convey their requirements and expectations? How can cus-tomer satisfaction monitoring look like? How can the working methods be followed up? The re-port is a case study that consists of qualitative data collected through received interviews and the implementation of a workshop. The result shows that the customer is in focus and and quality for company X means a satisfied customer through, for example, delivery of requested products in time at the right price. The dif-ferent respondents in the selection groups today have different working methods that are used to find out the customer's requirements and expectations. Customers are asked if they want to fill in a customer survey, which they rarely want. The process is not rooted in all parts of the organiza-tion from top to bottom. An improvement area in the company's process with customer follow-up has been identified, today two surveys with different scales are used and the company's quality objectives are calculated on one of the surveys. The study's conclusion is that the customer's pronounced, implicit and unconscious needs, espe-cially the latter, are of great importance for the experience of customer satisfaction. The needs may be identified by the SPIN model. Follow-up of customer satisfaction can be done through qualitative or quantitative measurements. The working methods can be followed up through the cornerstone model where all parts create a whole in offensive quality development and can work for a quality assurance of consulting services.

OBJETIVOS: Avaliar os efeitos da rubéola durante a gestação, sobre o feto, o recém-nascido e a criança. CASUÍSTICA E MÉTODO: Analisamos 35 gestantes com suspeita de rubéola que foram divididas em dois grupos. Grupo 1: 15 pacientes que apresentaram quadro clínico com comprovação sorológica. Grupo2: 20 pacientes com IgM positiva na rotina pré-natal, na ausência de quadro clínico. O seguimento ultrasonográfico mensal foi realizado em todas as pacientes e as do grupo 1 foram encaminhadas também para propedêutica invasiva. Foram também realizadas a ecocardiografia fetal e a Dopplervelocimetria. As placentas foram submetidas a exame anátomo-patológico. Os recém-nascidos vivos foram avaliados através de exame clínico e sorológico, além do potencial evocado auditivo, ultra-sonografia de crânio, fundo de olho e ecocardiografia pós-natal. RESULTADOS: No grupo 1: a infecção fetal ocorreu em 9 casos, sendo que o risco de transmissão vertical entre 2 a 14 semanas foi de 64,9%. A malformação ocorreu em 37,5% dos infectados. A ultrasonografia revelou crescimento intra-uterino retardado simétrico em todos os fetos infectados que atingiram o terceiro trimestre, tendo se iniciado, em média com 25,1 semanas. A cordocentese foi realizada em 9 pacientes e, todos os casos infectados, apresentavam IgM positiva e eritroblastose no sangue de cordão. A PCR no líquido amniótico foi positiva em todos os 3 casos em que ela foi realizada. 50% das placentas dos fetos infectados apresentava sinais sugestivos de infecção viral. A idade gestacional média do parto entre os infectados foi de 33,8 semanas e o peso médio ao nascimento foi 1365,6g.Todos os 6 nascidos-vivos infectados foram classificados como pequenos para a idade gestacional e apresentaram disacusia. A sobrevida entre os infectados, num seguimento pós-natal médio de 35,2 meses, foi de 62,5%. No grupo 2: a infecção não foi comprovada em nenhum dos recém-nascidos vivos, porém em um caso pudemos demonstrar a infecção congênita pelo vírus de Epstein-Barr. CONCLUSÕES: A transmissão vertical da rubéola no primeiro trimestre parece poder variar entre as populações, bem como a presença dos defeitos associados à infecção. Tanto o diagnóstico invasivo, como o ultrasonográfico apresentaram boa sensibilidade e especificidade. Pudemos estabelecer o padrão de crescimento fetal associado à infecção. A presença isolada de IgM positiva para rubéola na gestação não teve boa correlação com a presença de infecção neonatal, porém pode se associar à presença de outras infecções congênitas. / OBJECTIVES: Our aim was to analyse rubella effects on the fetus, new-born and child. MATERIAL AND METHODS: We analysed 35 patients with suspicious rubella during pregnancy. According to presence or absence of symptoms they were divided in two groups. Group 1: 15 patients presenting rash in which serology was positive. Grupo2: 20 symptomless patients found to have positive IgM during routine prenatal care. Monthly ultrasonographic evaluation was accomplished in all patients and in group 1 they were also offered prenatal invasive testing. Fetal echocardiography and Dopplers were performed. After birth, the placentas were submitted to pathological examination. The liveborn babies had clinical and serological examination. Auditory tests, brain scan, fundoscopy and postnatal echocardiography were also performed. RESULTS: In group 1: fetal infection occurred in 9 cases and vertical transmission between 2 to 14 weeks was 64,9%. Malformation was present in 37,5% of infected cases. Ultrasound revealed symmetrical intra-uterine growth retardation in all infected fetuses that reached the third trimester, and started around 25,1 weeks. Cordocentesis was accomplished in 9 cases and all the infected ones, presented positive IgM and erythroblastosis in cord blood. PCR in the amniotic fluid was positive in all 3 cases it was performed. 50% of the infected fetuses placentas presented signs of viral infection. The average gestacional age of delivery among infected cases was 33,8 weeks and medium birth weight was 1365,6g. All 6 liveborn infected babies were small for gestacional age and presented deafness. Survival among infected cases was 62,5%, medium follow-up was 35,2 months. In group 2: the infection was not demonstrated in any of neonates, although we could demonstrate a congenital infection caused by the Epstein-Barr virus. CONCLUSIONS: Vertical transmission of the rubella in the first trimester seems to vary among different populations, as well as the presence of the associated defects in the new-born. Invasive diagnosis and ultrasonographic follow-up presented good sensitivity and specificity. We could establish the pattern of fetal grown associated to the infection. The isolated presence of a positive rubella IgM in pregnancy did not correlated with congenital rubella, but it can be related to other congenital infections.

Vinte e seis pacientes com cardiomiopatia hipertrófica e fatores de risco de morte súbita, foram submetidos a implante de cardioversor-desfibrilador implantável de dupla-câmara, com seguimento médio de 19 meses. Observou-se quatro choques em arritmias letais, 4 pacientes apresentaram TVNS e 5 taquiarritmias supraventriculares. Ocorreu um óbito.Conclusões: Observamos: TPSV em 19,2%; TVNS em 15,4% e TVS/FV em 15,4%. Nenhuma variável clínica ou demográfica, discriminou o comportamento clínico ou funcional pós-implante de CDI; a recorrência de síncope pós implante de CDI, não se associou à presença de eventos arrítmicos e a hipertrofia maior que 30 mm se associou à choque precoce do CDI (p=0,003). / During 19 months of average follow-up period, we followed 26 patients with hypertrophic cardiomyopathy and high risk for sudden death, all treated by dual chamber implantable cardioverter-defibrillator. 4 patients had received appropriate ICD discharge, 4 patients with NSVT and 5 supraventricular arrhythmias. One death had occurred. Conclusions: we observed: supraventricular arrhythmias in 19,2%; NSVT in 15,4% and VT/VF in 15,4%. The clinical or demographic outcomes did not suggest any clinical or functional results after ICD implantation; syncope may occur after ICD implantation and no arrhythmias recordered by intracardiac electrograms and left-ventricular-wall thickness greater than 30 mm is associated with early ICD shocks (p=0,003).